Orphanet: Syndrome congenital d hamartome hypothalamique. Request PDF on ResearchGate | On Jul 1, , J. Mounach and others published Puberté précoce liée à un hamartome hypothalamique. Request PDF on ResearchGate | On May 1, , N. Ech-Cherif El Kettani and others published Hamartome hypothalamique révélant des crises gélastiques.

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You may thus request that your data, should it be inaccurate, incomplete, unclear, outdated, not be used or stored, be corrected, clarified, updated or deleted. An endoscopic procedure is performed under the general endotracheal anesthesia. Epileptic network of hypothalamic hamartoma: The depth electrode will guide the disconnection surgery as well as confirm the successful disconnection 28 Access to the PDF text. However, it did reveal a very important feature that sessile-type HHs usually cause GSs 1 Personal information regarding our website’s visitors, including their identity, is confidential.

Firing behavior and network activity of single neurons in human epileptic hypothalamic hamartoma. Because small HHs are often attached unilaterally, unilateral disconnection will be enough.

Puberté précoce liée à un hamartome hypothalamique – EM|consulte

GABAA receptor-mediated activation of L-type calcium channels induces neuronal excitation in surgically resected human hypothalamic hamartomas. Advances and Technical Standards in Neurosurgery. An optimal surgical approach should be selected based on the individual status of the lesion and the patient Fig.

Small hypothalamic hamartomas and gelastic seizures. Since Choi et al. Thorough preoperative investigation and the use of intraoperative stereotactic and electrophysiological guidance would ensure this goal Outline Masquer le plan. Personal information regarding our website’s visitors, including their identity, is confidential.


Electrophysiological properties of human hypothalamic hamartomas. Furthermore, they did not suggest any treatment strategy for Type 2 sessile HHs. Complications Transient short-term memory loss, weight gain, thalamic infarction with memory loss, and hemiparesis have been reported as hamartme complications.

The presence of these neurons constitute relevant evidence for ictogenesis of HH 3918 Surgical approaches to hypothalamic hamartomas. As per the Law relating to information storage and personal integrity, you have the right to oppose art 26 of that lawaccess art 34 of that law and rectify art 36 of that law your personal data.

Recently stereotactic laser ablation has been introduced and good seizure control has been achieved. An immediate seizure-free condition was the single most reliable factor for long-term seizure outcome.

Translation of “hypothalamus hamartome” in English

Routine scalp Hypohtalamique monitoring and long-term video-EEG monitoring, interictal and ictal 99 m-Tc hexamethylprophyleneamine oxime single photon emission computed tomography SPECTmagnetic resonance imaging MRIneuropsychological evaluation, ophthalmological assessments with perimetry, and endocrinological investigations are included.

Support Center Support Center. Cognitive functioning before and after surgical resection for hypothalamic hamartoma and epilepsy. Hypothalamic hamartoma with refractory epilepsy: When the thin pial membrane hypoghalamique arachnoid membrane is reached, dissection is complete.

Slit-like lateral ventricle and giant HHs within a 6-mm space of the third ventricle are no longer limitations in endoscopic disconnection Abilkassem bA.


hypothalamus hamartome – Translation into English – examples French | Reverso Context

Electric recording through depth electrode and transendoscopic intraoperative recording are also capable of recording the epileptic activities of HHs 21 Le syndrome hamartome hypothalaique J Neurol Neurosurg Psychiatry. Chabrol abF. Memory, endocrine function, behavior, and vision are potentially at risk after surgery 782327 Hypothalamic hamartomas associated with epilepsy: In bilateral attachment and giant HH cases, preoperative electrophysiological evaluation mostly revealed unilateral propagation of epileptiform discharge 31 The histopathology of hypothalamic hamartomas: As the nearby vicinity yamartome HHs consists of very critical structures, the utmost effort should be paid to reduce collateral damage.

Under direct visualization, the hamartoma can be coagulated by a monopolar electric coagulator or removed by microforceps Fig. Patients with most unilateral attachment, intraventricular type, and small HHs less than 1. However, most intraventricular HHs are excellent candidates for endoscopic resection or disconnection 823 Baizri cH.

If you are a subscriber, please sign in ‘My Account’ at the top right of the screen. If you want to subscribe to this journal, see our rates You can purchase hylothalamique item in Pay Per View: Relatively small ventricle and foramen of Monro. Disconnection of HHs from the hypothalamus with a monopolar coagulator. Delalande O, Fohlen M.